BookHaruhiko Sago, Hiroomi Okuyama, Yutaka Kanamori, editors.
Summary: This book offers readers a comprehensive understanding of congenital cystic lung disease based on a novel classification system recently proposed by leading researchers in the field. Presented in detail here, it includes various aspects, from fetal diagnosis and treatment to postnatal diagnosis and treatment, while also taking into account endoscopic surgical treatment and pathological diagnosis. Given the depth and breadth of its coverage, Congenital Cystic Lung Disease will be of interest not only to pediatric surgeons but also to pediatric respiratory physicians, neonatologists, and obstetricians engaged in fetal diagnosis and therapy, as well as pediatric radiologists and pathologists.
Contents:
Intro
Preface
Contents
1: Novel Classification of Congenital Cystic Lung Disease
1.1 Introduction
1.2 Novel Classification Based on the Embryology
1.3 Pathology Secondary to Lung Maldevelopment
1.4 Precise Definition of Each Entity of CCLD and Exclusion of the Unfit Lesions
1.5 Future Aspect of the Novel Classification
References
2: Epidemiology of Congenital Cystic Lung Disease: From Japan Nationwide Survey
2.1 Perinatal Clinical Features
2.2 Later Onset of Clinical Symptoms in Asymptomatic Neonates 2.3 Surgery, Complications, and Clinical Outcome
2.4 Respiratory Function Measured During Late Postoperative Period
2.5 Lung Lesions and Pathological Diagnosis
2.6 Discussion
References
3: Fetal Diagnosis and Therapy for Congenital Cystic Lung Disease
3.1 Introduction
3.2 Prenatal Diagnosis of CLCD
3.2.1 Origin of the Blood Supply
3.2.2 Appearance of the Lung Cyst
3.2.3 Lung Cystic Lesion Size
3.2.4 Presence of Hydrops and Changes in the Appearance
3.3 Fetal Therapy
3.3.1 TAS
3.3.2 Fetal Surgical Resection
3.3.3 Maternal Steroid Therapy 3.3.4 Other Fetal Therapies
References
4: Fetal Diagnostic Imaging of Congenital Cystic Lung Disease
4.1 Introduction
4.2 Safety, Magnetic Fields, and Gestational Age in Fetal MRI
4.3 Fetal MR Image Acquisition Technique and Normal Lung Anatomy
4.4 Image Findings
4.4.1 Congenital Pulmonary Airway Malformation (CPAM)
4.5 Bronchopulmonary Sequestration (BPS)
4.6 Bronchial Atresia (BA)
4.7 Congenital Lobar Emphysema (CLE)
4.8 Congenital Bronchogenic Cyst
4.9 Summary
References
5: Perinatal Care for Severe Congenital Pulmonary Airway Malformation 5.1 Introduction
5.2 Prenatal Management and Clinical Course
5.2.1 Classification Based on Pathological Findings and Fetal Sonographic Appearance
5.2.2 Evaluation of Cystic Lesion Size Using Fetal Ultrasonography
5.2.3 Treatment of Fetuses with CPAM
5.2.4 Response to Fetal Treatment and Condition Just Before Birth
5.3 Management of Neonates with CPAM at Birth and Infancy
5.3.1 Emergency Surgery Strategy
5.3.2 Points and Pitfalls of Each Department's Role in Emergency Surgery Strategy for Neonates with Severe CPAM 5.3.2.1 Department of Obstetrics for Fetal Medicine
5.3.2.2 Department of Neonatology
5.3.2.3 Department of Anesthesia
5.3.2.4 Department of Surgery
5.4 Management of Patients with CPAM in Infancy and Childhood
5.5 Discussion and Future Perspective
References
6: Postnatal Imaging Diagnosis of Congenital Cystic Lung Disease
6.1 Introduction
6.2 Diagnostic Modalities
6.2.1 Chest Radiography
6.2.2 Computed Tomography: CT
6.2.3 Magnetic Resonance Imaging: MRI
6.2.4 Ultrasound: US
6.3 Bronchial Obstruction
6.3.1 Congenital Bronchial Atresia